Cerebellar Degenerations Book

	Contributing authors
	Preface
	Introduction
1	The cerebellum and its disorders in the dawn of the molecular age	1
I	Basic Neurosciences of the Cerebellum
2	Anatomy and neurochemical anatomy of the cerebellum	11
3	Physiology of the cerebellum	59
4	Amino acid transmitters in the adult and developing cerebellum	89
5	Glutamate receptors in mammalian cerebellum: Alterations in human ataxic disorders and cerebellar mutant mice	123
6	Regional and cellular distribution of glutamate dehydrogenase and pyruvate dehydrogenase complex in brain: Implications for neurodegenerative disorders	139
7	The Purkinje cell degeneration mutant: a model to study the consequences of neuronal degeneration	159
II	Clinical Neurosciences of the Cerebellum
8	Classification and epidemiology of cerebellar degenerations	185
9	The cerebellar cortex and the dentate nucleus in hereditary ataxia	205
10	Clinical neurophysiology in olivopontocerebellar atrophy	237
11	Pathophysiology of ataxia in humans	261
12	Oculomotor abnormalities in cerebellar degeneration	281
13	Clinical and radiologic features of cerebellar degeneration	305
III	Etiopathogenesis of Cerebellar Disorders
14	Glutamate dehydrogenase deficiency in cerebellar degenerations	369
15	Mitochondrial abnormalities in hereditary ataxias	391
16	Cerebellar disorder in the hexosaminidase deficiencies	403
17	Dominant olivopontocerebellar atrophy mapping to human chromosome 6p	425
18	Positron emission tomography studies of cerebellar degeneration	443
19	Ataxia telengiectasia: A human model of neuroimmune degeneration	461
20	Paraneoplastic cerebellar degeneration	475
	Index	499